Abstract:
Pediatric hiatal hernia is a rare congenital anomaly with congenital giant hiatal hernia being the rarest subtype. The congenital giant hiatal hernia has never been reported to contain pancreas. We report an extremely rare case of congenital giant hiatal hernia presented with respiratory distress and rapid deterioration of the respiratory function. The patient was found to have unreported intraoperative findings of colon and pancreas hiatal sac contents. Congenital giant hiatal hernia requires prompt intervention largely due to the risk of morbidity and mortality. The best option for management is surgical repair with an open or laparoscopic approach.
